It believe it can be considered in selected paients with a mild or absent sensorineural hearing loss. As in most patients there is a development of a significative sensorineural component in later stages of the disease, the osteointegrated implants may not be the best option.

It depends on the type of OI. Biggest issue is long-term failure of osteointegration as the bone quality deteriorates.

I agree that it depends on the type of OI. In most series of stapedectomies in OI the patients are mainly in the group of type I disease. In type III OI, the severe type,demineralization of the ossicles is worse and the result of stapedectomy probably is poorer, although, the are no reports, as our knowledge, on stapes surgery in these patients. If a patient refuses stapes surgery and is poorly adapted to the hearing aids, preferring to carry out BAHA surgery despite knowing the risks of poor osseointegration for his disease, and hearing loss is not progressing rapidly with age I think we should consider this treatment option.

Successful bone-anchored hearing aid implantation in a patient with osteogenesis imperfecta

Article in The Journal of Laryngology & Otology 129(11):1-4 · September 2015

DOI: 10.1017/S0022215115002510